ATI RN
Pediatric Musculoskeletal Disorders Quizlet Questions
Question 1 of 5
The term congenital muscular dystrophy is misleading because all muscular dystrophies are genetically determined. A distinguishing feature of the congenital dystrophies from other muscular dystrophies, is a high association with malformations of
Correct Answer: C
Rationale: Congenital muscular dystrophies, such as Fukuyama type, are notably associated with brain malformations like lissencephaly or polymicrogyria.
Question 2 of 5
Miller-Fisher syndrome (MFS) consists of acute external and occasionally internal ophthalmoplegia, ataxia, and areflexia. Of the following, the MOST likely cranial nerve involved is
Correct Answer: A
Rationale: The 3rd cranial nerve (oculomotor) is most commonly involved in MFS, causing ophthalmoplegia.
Question 3 of 5
Bell palsy usually develops abruptly about 2 wk after a systemic viral infection. Of the following, the MOST common viral cause is
Correct Answer: D
Rationale: Herpes simplex virus is the most commonly implicated viral trigger for Bell palsy, likely via reactivation.
Question 4 of 5
Of the following, the LEAST recognized presentation of Charcot-Marie-Tooth disease is
Correct Answer: B
Rationale: Claw hand is less commonly highlighted as a presentation of CMT compared to foot drop, pes cavus, or stork-like legs.
Question 5 of 5
Malignant hyperthermia is an acute hypermetabolic syndrome that is triggered by inhalational anesthetic agents and succinylcholine. Of the following, which myopathy is consistently associated with malignant hyperthermia?
Correct Answer: A
Rationale: Central core myopathy is consistently associated with malignant hyperthermia due to RYR1 gene mutations.