ATI RN
Pediatric Integumentary Questions Questions
Question 1 of 5
Redundant skin over the posterior part of the neck is common in the following syndromes EXCEPT
Correct Answer: A
Rationale: Ehlers-Danlos syndrome is characterized by hyperelastic skin, not redundant neck skin. Turner, Noonan, and Down syndromes often feature neck webbing or redundancy, making A the exception.
Question 2 of 5
Ataxia-telangiectasia is transmitted as an autosomal recessive trait; the characteristic telangiectasias develop at approximately 3 yr of age, first on
Correct Answer: A
Rationale: In ataxia-telangiectasia, telangiectasias typically first appear on the bulbar conjunctivae around age 3-6, making A correct.
Question 3 of 5
The following syndrome has a strong association with Café-au-lait spots
Correct Answer: B
Rationale: McCune-Albright syndrome is strongly associated with café-au-lait spots, often large and irregular, making B correct.
Question 4 of 5
Erythema multiforme (EM) is characterized by an abrupt, symmetric cutaneous eruption, MOST commonly on the
Correct Answer: D
Rationale: Erythema multiforme typically involves the palms and soles with target lesions, making D correct.
Question 5 of 5
Severe mucosal blistering; GI involvement; laryngeal involvement (airway obstruction); and urologic involvement are the extracutaneous clinical features of
Correct Answer: C
Rationale: Junctional epidermolysis bullosa-Herlitz type (AR) is severe, with widespread blistering and extracutaneous involvement like GI and laryngeal issues, making C correct.