ATI RN
Pediatric Immunization NCLEX Questions Ricci Questions
Question 1 of 5
Neutropenia is noted in children in all of the following conditions EXCEPT
Correct Answer: D
Rationale: Hunter syndrome (MPS II) is a lysosomal storage disorder not typically associated with neutropenia. Kostmann disease (severe congenital neutropenia), viral infections, and maternal preeclampsia can all cause neutropenia through various mechanisms affecting neutrophil production or survival.
Question 2 of 5
A child is found to have a normal WBC count but serum concentrations of IgG, IgA, IgM, and IgE below the 95% lower limits for age. Which is the most likely diagnosis?
Correct Answer: D
Rationale: Common variable immunodeficiency (CVID) is characterized by low levels of multiple immunoglobulin classes (IgG, IgA, IgM) with normal WBC, often presenting later in childhood.
Question 3 of 5
A 4-month-old female presents with diarrhea and malabsorption, and on initial laboratory testing has a WBC count of 900/mm³. Which of the following is the most likely diagnosis?
Correct Answer: D
Rationale: Severe combined immunodeficiency (SCID) presents with severe lymphopenia (WBC 900) and early infections or failure to thrive, like diarrhea, due to absent T and B cell function.
Question 4 of 5
Selective IgA deficiency is defined as serum IgA levels less than 10 mg/dL with normal levels of other immunoglobulins. The diagnosis cannot be confirmed until the patient is at least
Correct Answer: B
Rationale: IgA levels may not fully mature until after infancy, so diagnosis is typically confirmed after 4 years of age when levels should stabilize.
Question 5 of 5
A 5-month-old infant presented with reluctance to feed, lethargy, abdominal distension, and severe gingivitis. The parents are healthy relatives and give history of non-purulent omphalitis with separation of umbilical stump at the age of 2 months. His peripheral smear showed neutrophil count 24,000/mm3. Of the following, the MOST effective life saving measure is
Correct Answer: C
Rationale: Stem cell transplantation corrects leukocyte adhesion deficiency, addressing the underlying genetic defect for long-term survival.