ATI RN
Pediatric Endocrine Nursing Questions Questions
Question 1 of 5
Matching: Peroxisomal disorder
Correct Answer: A
Rationale: All listed conditions (e.g., Zellweger) are peroxisomal disorders.
Question 2 of 5
Matching: Lipidosis - Sandhoff
Correct Answer: C
Rationale: Sandhoff disease has both cherry red spot and hepatosplenomegaly.
Question 3 of 5
Treatment of the patient in the previous two questions is best achieved with
Correct Answer: B
Rationale: Enzyme replacement with β-glucosidase (e.g., imiglucerase) treats Gaucher disease.
Question 4 of 5
Matching: Glycogen storage diseases - Anderson
Correct Answer: D
Rationale: Anderson (type IV) causes cirrhosis and failure to thrive.
Question 5 of 5
Typical insulin dosage requirement in prepubertal children after the 'honeymoon' period is
Correct Answer: D
Rationale: Post-honeymoon, prepubertal children with type 1 DM typically require 0.7-1 U/kg/day; 0.7 (D) is the most common average.