Emery-Dreifuss Muscular Dystrophy (scapuloperoneal or scapulohumeral muscular dystrophy) is a rare X-linked recessive dystrophy. Of the following, the MOST characteristic feature is

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Pediatric Musculoskeletal Disorders NCLEX Questions Questions

Question 1 of 5

Emery-Dreifuss Muscular Dystrophy (scapuloperoneal or scapulohumeral muscular dystrophy) is a rare X-linked recessive dystrophy. Of the following, the MOST characteristic feature is

Correct Answer: D

Rationale: Dilated cardiomyopathy, along with early contractures and humeroperoneal weakness, is a hallmark of Emery-Dreifuss muscular dystrophy.

Question 2 of 5

In Guillain-Barré syndrome, the paralysis usually follows a nonspecific gastrointestinal or respiratory infection by approximately 10 days. Of the following, the MOST likely respiratory infection that triggers the disease is

Correct Answer: D

Rationale: Mycoplasma pneumoniae is a well-documented respiratory trigger for Guillain-Barré syndrome, often linked to autoimmune responses.

Question 3 of 5

In Guillain-Barré syndrome, respiratory effort must be monitored to prevent respiratory failure and respiratory arrest. Of the following, the MOST recognized sign of impending respiratory failure is

Correct Answer: B

Rationale: Tachypnea is a key sign of impending respiratory failure in GBS, indicating compensatory effort for weakened respiratory muscles.

Question 4 of 5

Bell palsy is an acute unilateral peripheral facial nerve palsy that is not associated with other cranial neuropathies or brainstem dysfunction. Of the following, the MOST traditional treatment is

Correct Answer: B

Rationale: Prednisone is the most traditional and evidence-based treatment for Bell palsy to reduce inflammation and improve recovery.

Question 5 of 5

All the following are preserved in Charcot-Marie-Tooth disease EXCEPT

Correct Answer: B

Rationale: Tibial nerves are not preserved in CMT; they are commonly affected, contributing to distal leg weakness.

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