ATI LPN
Wong's Essentials of Pediatric Nursing 11th Edition Test Bank
Chapter 24 : The Child with Hematologic or Immunologic Dysfunction Questions
Question 1 of 5
What statement best describes b-thalassemia major (Cooley anemia)?
Correct Answer: C
Rationale: B-thalassemia major has a higher incidence in Mediterranean populations and is inherited, not acquired. It involves overproduction of unstable RBCs, not inadequate numbers, and is distinct from sickle cell anemia, which is common in West African populations.
Question 2 of 5
What therapeutic intervention is most appropriate for a child with b-thalassemia major?
Correct Answer: D
Rationale: Frequent blood transfusions maintain hemoglobin above 9.5 g/dl to prevent bone marrow expansion in b-thalassemia major. Oxygen and hydration are supportive but not primary, and supplemental iron is harmful due to existing iron overload from transfusions.
Question 3 of 5
Iron overload is a side effect of chronic transfusion therapy. What treatment assists in minimizing this complication?
Correct Answer: B
Rationale: Deferoxamine infusions chelate and excrete excess iron, minimizing overload from chronic transfusions. Magnetic therapy is ineffective, hemoglobin electrophoresis is diagnostic, and washing RBCs removes other components, not iron.
Question 4 of 5
In which condition are all the formed elements of the blood simultaneously depressed?
Correct Answer: A
Rationale: Aplastic anemia involves bone marrow failure, depressing all blood elements (RBCs, WBCs, platelets). Sickle cell anemia affects hemoglobin, thalassemia major impacts hemoglobin chain production, and iron deficiency reduces RBC size and hemoglobin, not all elements.
Question 5 of 5
For children who do not have a matched sibling bone marrow donor, the therapeutic management of aplastic anemia includes what intervention?
Correct Answer: D
Rationale: Immunosuppressive therapy (e.g., antilymphocyte globulin, cyclosporine) treats aplastic anemia, likely an autoimmune condition, improving prognosis. Antibiotics treat infections, not the condition; antiretrovirals and iron are irrelevant to aplastic anemia management.